restrictive dermopathy (MONDO_0031213) is a congenital genodermatosis with skin/mucosae involvement, characterized by very tight and thin skin with erosions and scaling, associated to a typical facial dysmorphism, arthrogryposis multiplex, fetal akinesia or hypokinesia deformation sequence (FADS) and pulmonary hypoplasia without neurological abnormalities. Also known as: lethal hyperkeratosis-contracture syndrome, lethal restrictive dermopathy, lethal tight skin-contracture syndrome, tight skin contracture syndrome.