Monarch Disease Ontology id MONDO_0100135 (Dravet syndrome) is a channelopathy with epilepsy of with onset during the first year of life, typically 4-5 months, characterized by status epilepticus and a variety of drug-resistant seizures often induced by fever, presenting in previously healthy children, and which frequently leads to cognitive and motor impairment. Dravet differs from other channelopathies usually due to a mutation in SCN1A. Also known as: DS, Dravet, SME, SMEB, myoclonic epilepsy, severe, of infancy, severe myoclonic epilepsy of infancy.