Bazex-Dupre-Christol syndrome is a rare genodermatosis with a predisposition to early-onset basal cell carcinomas. The disease is Orphanet rare-disease nomenclature entry Orphanet_113 (Bazex-Dupré-Christol syndrome). Also known as: BDCS, Bazex-Dupre-Christol syndrome, follicular atrophoderma and basal cell carcinomas.