Cutis gyrata - acanthosis nigricans - craniosynostosis (Orphanet_1555) is cutis Gyrata - Acanthosis nigricans - craniosynthosis also known as Beare-Stevenson syndrome (BSS) is a rare autosomal dominant disorder characterized by cutis gyrata, craniosynostosis, acanthosis nigricans, anogenital anomalies, and an intellectual disability. Also known as: Beare-Stevenson cutis gyrata syndrome.