Orphanet_183678 (Hermansky-Pudlak syndrome with neutropenia) can be described as follows. Hermansky-Pudlak syndrome type 2 (HPS-2) is a type of Hermansky-Pudlak syndrome (HPS; see this term), a multi-system disorder characterized by oculocutaneous albinism, bleeding diathesis and neutropenia. Also known as: HPS2, Hermansky-Pudlak syndrome type 2.