Pulmonary capillary hemangiomatosis (PCH) is a rare form of pulmonary arterial hypertension (PAH, see this term) characterized by a capillary infiltration of the pulmonary interstitium, bronchioles and pleura leading to elevated pulmonary arterial resistance and right heart failure. PCH is potentially fatal. The disease is Orphanet_199241 (Pulmonary capillary hemangiomatosis).