Progressive sensorineural hearing loss - hypertrophic cardiomyopathy is an extremely rare disorder described in one family to date that is characterized by progressive, late onset, autosomal dominant sensorineural hearing loss, QT interval prolongation, and mild cardiac hypertrophy. The disease is Progressive sensorineural hearing loss - hypertrophic cardiomyopathy (Orphanet_228012, an Orphanet rare-disease nomenclature id). Also known as: Progressive neurosensory deafness - hypertrophic cardiomyopathy, Progressive neurosensory hearing loss - hypertrophic cardiomyopathy, Progressive sensorineural deafness - hypertrophic cardiomyopathy.