Orphanet_2314 (Autosomal dominant hyper-IgE syndrome) is 2000 IU/ml), recurring staphylococcal skin abscesses, and recurrent pneumonia with formation of pneumatoceles. Also known as: AD-HIES, Autosomal dominant HIES, Autosomal dominant hyperimmunoglobulin E syndrome, Buckley syndrome, Hyperimmunoglobulin E syndrome type 1, Hyperimmunoglobulin E-recurrent infection syndrome, Job syndrome, STAT3 deficiency.