Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is a heart muscle disease that consists in progressive dystrophy of primarily the right ventricular myocardium with fibro-fatty replacement and ventricular dilation, and that is clinically characterized by ventricular arrhythmias. and progressive right ventricular or biventricular failure. ARCVD is a major cause of sudden death in the young and among athletes. The disease is Orphanet_247 (Arrhythmogenic right ventricular dysplasia). Also known as: ARVC, ARVD, Arrhythmogenic right ventricular cardiomyopathy.