Linear nevus sebaceous syndrome (LNSS) is characterized by the association of a large sebaceous nevus, usually appearing on the face or on the scalp, with a broad spectrum of abnormalities that may affect every organ system, including the central nervous system (brain neoplasms, hemimegalencephaly and lateral ventricle enlargement). The disease is Linear nevus sebaceus syndrome (Orphanet rare-disease nomenclature entry Orphanet_2612). Also known as: Nevus sebaceous of Jadassohn, Nevus sebaceus of Jadassohn, Nevus sebaceus syndrome, Schimmelpenning syndrome, Solomon syndrome, linear nevus sebaceus syndrome, linear sebaceous Nevus, organoid Nevus.