Osteopathia striata with cranial sclerosis (OS-CS) is a bone dysplasia characterized by longitudinal striations of the metaphyses of the long bones, sclerosis of the craniofacial bones, macrocephaly, cleft palate and hearing loss. The disease is Osteopathia striata - cranial sclerosis (Orphanet_2780). Also known as: Hyperostosis generalisata with striations, Robinow-Unger syndrome.