Distal arthrogryposis type 4 is an inherited developmental defect syndrome characterized by multiple congenital contractures of limbs, without primary neurologic and/or muscle disease that affects limb function, and a mild to severe scoliosis. Intelligence is normal. The disease is Arthrogryposis - severe scoliosis (Orphanet_65720). Also known as: Distal arthrogryposis type 4, Distal arthrogryposis type IID.