Autosomal dominant cerebellar ataxia (ADCA) type 1 is a group of spinocerebellar ataxias (SCAs) characterized by ataxia with other neurological signs, including oculomotor disturbances, cognitive deficits, pyramidal and extrapyramidal dysfunction, bulbar, spinal and peripheral nervous system involvement. The disease is Orphanet rare-disease nomenclature entry Orphanet_94145 (Autosomal dominant cerebellar ataxia type 1). Also known as: ADCA1, ADCAI, Autosomal dominant cerebellar ataxia type I, Cerebellar plus syndrome.